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Submitted: 18 September 2019 Modified: 18 September 2019
HERDIN Record #: 100731-19091811084034

Tricuspid valve atresia and Bjork procedure, a biventricular repair.

Rochelle R. Pamaran,
Glenda T. Tubianosa

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Introduction: Tricuspid Valve Atresia consists of complete agenesis of the tricuspid valve and absence of a direct communication between the right atrium and the right ventricle. It constitutes 2.7% of all congenital heart disease and occurs in approximately 1:15,000 live births.1 Surgical approach for tricuspid atresia is done in three stages. Blalock Taussig shunt soon after birth or pulmonary artery band depending on the size of the ventricular septal defect (VSD) and the main pulmonary artery, Glenn surgery (bidirectional cavopulmonary shunt) at 3-6 months of age, and Fontan surgery at 2-3 years.2


Case: We report a case of 21 years old, female who underwent Pulmonary artery banding and bidirectional Glenn Shunt (Bjork Procedure) at 2 years old and placement of RA to RV anastomic conduit at 5 years old. The patient tolerated each procedure well and is now a grown-up child with no functional limitation.


Conclusion: Bjork surgery for Tricuspid Valve Atresia with normally related great arteries, Large VSD with normal Pulmonary valve gives the advantages of RV growth, biventricular function and good outcome without any medication.

Publication Type
Research Project
Date
January 1-September 18, 2019
LocationLocation CodeAvailable FormatAvailability
Philippine Heart Center Medical Library CR.006.19 Fulltext Print Format